| 基因名 | MCCC1 |
| 英文全称 | Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial |
| 别称 | MCC B, MCCA, MCCase subunit alpha, MCCC1 |
| 中文名称 | 甲基巴豆酰辅酶A羧化酶亚基α,线粒体 |
| Uniprot | Q96RQ3 |
| GeneID | 56922 |
| 交叉反应(推测) | Human Mouse Rat |
| 氨基酸大小 | 39kDa |
| 表达氨基酸 | 376-725aa |
| Background | This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase.This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA.Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. |
| Application | Immunology research |
| Derived from | E.coli |
| Purification | NI-NTA affinity purification |
| Formulation | Lyophilized from a 0.2 μm filtered solution of Tris-HCl, PH8.0. |
| Shipping | The product is shipped at -20°C temperature. Upon receipt, store it immediately at the temperature listed below. |
| Storage | Reconstituted protein solution can be stored at 4-7°C for 1-2 months, stable at < -20°C for 2-3 years. |
| Reconstitution | Reconstituted protein solution can be diluted with distilled PBS. Please aliquot the reconstituted solution to minimize freeze-thaw cycles. |
| Purity | Purity≥85% as determined by reducing SDS-PAGE. |
| 规格 | 10ug 50ug 100ug 1mg |